Angioimmunoblastic lymphadenopathy with dysproteinemia
نویسندگان
چکیده
منابع مشابه
Successful treatment of angioimmunoblastic lymphadenopathy with dysproteinemia with fludarabine.
Angioimmunoblastic lymphadenopathy with dysproteinemia (AILD) is a rare lymphoproliferative disorder that occurs predominantly in older adults and is characterized by generalized lymphadenopathy, hepatosplenomegaly, fever, and a pruritic skin rash. Patients often have hypergammaglobulinemia, autoantibodies, and hemolytic anemia. The diagnosis requires a lymph node biopsy showing effacement of t...
متن کاملCutaneous involvement in patients with angioimmunoblastic lymphadenopathy with dysproteinemia: a clinical, immunohistological, and molecular analysis.
OBJECTIVE To determine whether cutaneous involvement in patients with angioimmunoblastic lymphadenopathy with dysproteinemia (AILD) is related to a clonal T-cell proliferation. DESIGN Retrospective study. SETTING University hospitals. PATIENTS Ten patients with AILD and cutaneous involvement. MAIN OUTCOME MEASURE The T-cell receptor-gamma (TCRG)gene rearrangement was studied with the us...
متن کاملPolyarthritis and angioimmunoblastic lymphadenopathy.
Angioimmunoblastic lymphadenopathy (AILD) is a lymphoproliferative disorder with well established clinical and histological features, one of the clinical manifestations being a peripheral polyarthritis. A case of AILD with a symmetrical non-erosive peripheral polyarthritis is described, including the findings in the synovial fluid and histology of the synovium. There was a marked reduction in t...
متن کاملHypercalcaemia and angioimmunoblastic lymphadenopathy
A 57-year-old woman presented in November 1978 with a two-month history of intermittent fever, an evanescent non-pruritic rash, loss of 10 kg, and generalised lymphadenopathy and hepatosplenomegaly. Haemoglobin concentration was 7 8 g/dl, white cell count 316 x 109/1 (31 600/mm3), and platelet count 142 x 109/1. Erythrocyte sedimentation rate was 102 mm in first hour (Westergren), and Coombs te...
متن کاملArthritis and angioimmunoblastic lymphadenopathy.
We report 2 contrasting cases of a seronegative polyarthritis associated with angioimmunoblastic lymphadenopathy (AILD). Both cases were nonerosive, with symmetrical involvement of the elbows, wrists, knees, and ankles. In one the arthritis appeared concurrently with the main systemic manifestations of AILD. The second presented with polyarthritis 18 months before the onset of AILD. This patien...
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ژورنال
عنوان ژورنال: Cancer
سال: 1977
ISSN: 0008-543X,1097-0142
DOI: 10.1002/1097-0142(197711)40:5<2152::aid-cncr2820400525>3.0.co;2-k